{"id":727,"date":"2020-12-25T00:00:00","date_gmt":"2020-12-24T15:00:00","guid":{"rendered":"https:\/\/m.kawasaki-m.ac.jp\/mgm-lyso\/?p=727"},"modified":"2026-02-04T11:39:26","modified_gmt":"2026-02-04T02:39:26","slug":"%e5%9b%bd%e9%9a%9b%e4%ba%a4%e6%b5%81%e5%8d%94%e5%ae%9a%e3%82%92%e7%b7%a0%e7%b5%90%e3%81%97%e3%81%be%e3%81%97%e3%81%9f","status":"publish","type":"post","link":"https:\/\/m.kawasaki-m.ac.jp\/mgm-lyso\/?p=727","title":{"rendered":"\u56fd\u969b\u4ea4\u6d41\u5354\u5b9a\u3092\u7de0\u7d50\u3057\u307e\u3057\u305f"},"content":{"rendered":"\n<p class=\"has-black-color has-text-color wp-block-paragraph\">\u79c1\u305f\u3061\u306f\u30ed\u30b7\u30a2\u5317\u6771\u9023\u90a6\u5927\u5b66\uff08\u30e4\u30af\u30fc\u30c4\u30af\uff09\u3068\u306e\u5171\u540c\u7814\u7a76\u306b\u304a\u3044\u3066\u3001\u65b0\u3057\u3044\u75be\u60a3\uff08Mucopolysaccharidosis-Plus Syndrome, MPSPS\uff09\u3092\u540c\u5b9a\u3057\u307e\u3057\u305f\uff08<span style=\"text-decoration: underline;\"><a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/28013294\/\">Kondo H, <em>et al.<\/em> <strong><em>Hum Mol Genet<\/em><\/strong> 2017<\/a><\/span>, OMIM <a href=\"https:\/\/www.omim.org\/entry\/617303\"><span style=\"text-decoration: underline;\">#617303<\/span><\/a>\uff09\u3002<br><br>\u5f15\u304d\u7d9a\u304d\u672c\u75be\u60a3\u306e\u5206\u5b50\u30e1\u30ab\u30cb\u30ba\u30e0\u306e\u89e3\u660e\u3084\u6cbb\u7642\u6cd5\u306e\u958b\u767a\u3092\u9032\u3081\u3066\u3044\u304f\u305f\u3081\u306b\u3001\u3053\u306e\u5ea6\u5927\u5b66\u9593\u306e\u5b66\u8853\u4ea4\u6d41\u5354\u5b9a\u3092\u7de0\u7d50\u3057\u307e\u3057\u305f\u3002<br><br>\u65e5\u672c\u5b66\u8853\u632f\u8208\u4f1a\u30fb\u5916\u56fd\u4eba\u7279\u5225\u7814\u7a76\u54e1\uff08Filipp Vasilev\u3055\u3093\uff09\u3001\u6587\u90e8\u79d1\u5b66\u7701\u30fb\u56fd\u8cbb\u7559\u5b66\u751f\uff08Viktoriia Sofronova\u3055\u3093\uff09\u304c\u5317\u6771\u9023\u90a6\u5927\u5b66\u304b\u3089\u5f53\u6559\u5ba4\u306b\u7559\u5b66\u3055\u308c\u3066\u672c\u75be\u60a3\u306e\u7814\u7a76\u306b\u643a\u308f\u3063\u3066\u3044\u307e\u3059\u3002<br><br><span style=\"text-decoration: underline;\"><a href=\"https:\/\/www.s-vfu.ru\/news\/detail.php?SECTION_ID=17&amp;ELEMENT_ID=146413\">\u5317\u6771\u9023\u90a6\u5927\u5b66\u306e\u30cb\u30e5\u30fc\u30b9\u30ea\u30ea\u30fc\u30b9<\/a><\/span>\uff1c\u5916\u90e8\u30b5\u30a4\u30c8\uff1e<\/p>\n\n\n\n<div class=\"wp-block-group\"><div class=\"wp-block-group__inner-container is-layout-flow wp-block-group-is-layout-flow\">\n<div class=\"wp-block-columns is-layout-flex wp-container-core-columns-is-layout-8f761849 wp-block-columns-is-layout-flex\">\n<div class=\"wp-block-column is-layout-flow wp-block-column-is-layout-flow\" style=\"flex-basis:100%\">\n<div class=\"wp-block-group\"><div class=\"wp-block-group__inner-container is-layout-flow wp-block-group-is-layout-flow\">\n<div class=\"wp-block-columns is-layout-flex wp-container-core-columns-is-layout-8f761849 wp-block-columns-is-layout-flex\">\n<div class=\"wp-block-column is-layout-flow wp-block-column-is-layout-flow\" style=\"flex-basis:100%\">\n<figure class=\"wp-block-gallery columns-2 is-cropped wp-block-gallery-1 is-layout-flex wp-block-gallery-is-layout-flex\"><ul class=\"blocks-gallery-grid\"><li class=\"blocks-gallery-item\"><figure><img loading=\"lazy\" decoding=\"async\" width=\"724\" height=\"1024\" src=\"https:\/\/m.kawasaki-m.ac.jp\/mgm-lyso\/wp-content\/uploads\/2021\/09\/134-0-724x1024.jpg\" alt=\"\" data-id=\"740\" data-link=\"https:\/\/m.kawasaki-m.ac.jp\/mgm-lyso\/?attachment_id=740\" class=\"wp-image-740\" srcset=\"https:\/\/m.kawasaki-m.ac.jp\/mgm-lyso\/wp-content\/uploads\/2021\/09\/134-0-724x1024.jpg 724w, https:\/\/m.kawasaki-m.ac.jp\/mgm-lyso\/wp-content\/uploads\/2021\/09\/134-0-212x300.jpg 212w, https:\/\/m.kawasaki-m.ac.jp\/mgm-lyso\/wp-content\/uploads\/2021\/09\/134-0.jpg 744w\" sizes=\"auto, (max-width: 724px) 100vw, 724px\" \/><\/figure><\/li><li class=\"blocks-gallery-item\"><figure><img loading=\"lazy\" decoding=\"async\" width=\"724\" height=\"1024\" src=\"https:\/\/m.kawasaki-m.ac.jp\/mgm-lyso\/wp-content\/uploads\/2021\/09\/134-3-724x1024.jpg\" alt=\"\" data-id=\"741\" data-full-url=\"https:\/\/m.kawasaki-m.ac.jp\/mgm-lyso\/wp-content\/uploads\/2021\/09\/134-3.jpg\" data-link=\"https:\/\/m.kawasaki-m.ac.jp\/mgm-lyso\/?attachment_id=741\" class=\"wp-image-741\" srcset=\"https:\/\/m.kawasaki-m.ac.jp\/mgm-lyso\/wp-content\/uploads\/2021\/09\/134-3-724x1024.jpg 724w, https:\/\/m.kawasaki-m.ac.jp\/mgm-lyso\/wp-content\/uploads\/2021\/09\/134-3-212x300.jpg 212w, https:\/\/m.kawasaki-m.ac.jp\/mgm-lyso\/wp-content\/uploads\/2021\/09\/134-3.jpg 744w\" sizes=\"auto, (max-width: 724px) 100vw, 724px\" \/><\/figure><\/li><\/ul><figcaption class=\"blocks-gallery-caption\">\uff1c\u5ddd\u5d0e\u533b\u79d1\u5927\u5b66\u5b66\u5831134\u53f7\u3088\u308a\uff1e<\/figcaption><\/figure>\n<\/div>\n<\/div>\n<\/div><\/div>\n<\/div>\n<\/div>\n<\/div><\/div>\n","protected":false},"excerpt":{"rendered":"<p>\u79c1\u305f\u3061\u306f\u30ed\u30b7\u30a2\u5317\u6771\u9023\u90a6\u5927\u5b66\uff08\u30e4\u30af\u30fc\u30c4\u30af\uff09\u3068\u306e\u5171\u540c\u7814\u7a76\u306b\u304a\u3044\u3066\u3001\u65b0\u3057\u3044\u75be\u60a3\uff08Mucopolysaccharidosis-Plus Syndrome, MPSPS\uff09\u3092\u540c\u5b9a\u3057\u307e\u3057\u305f\uff08Kondo H, et al. Hum Mo&hellip;<\/p>\n","protected":false},"author":1,"featured_media":0,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[4],"tags":[],"class_list":["post-727","post","type-post","status-publish","format-standard","hentry","category-4"],"_links":{"self":[{"href":"https:\/\/m.kawasaki-m.ac.jp\/mgm-lyso\/index.php?rest_route=\/wp\/v2\/posts\/727","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/m.kawasaki-m.ac.jp\/mgm-lyso\/index.php?rest_route=\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/m.kawasaki-m.ac.jp\/mgm-lyso\/index.php?rest_route=\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/m.kawasaki-m.ac.jp\/mgm-lyso\/index.php?rest_route=\/wp\/v2\/users\/1"}],"replies":[{"embeddable":true,"href":"https:\/\/m.kawasaki-m.ac.jp\/mgm-lyso\/index.php?rest_route=%2Fwp%2Fv2%2Fcomments&post=727"}],"version-history":[{"count":6,"href":"https:\/\/m.kawasaki-m.ac.jp\/mgm-lyso\/index.php?rest_route=\/wp\/v2\/posts\/727\/revisions"}],"predecessor-version":[{"id":743,"href":"https:\/\/m.kawasaki-m.ac.jp\/mgm-lyso\/index.php?rest_route=\/wp\/v2\/posts\/727\/revisions\/743"}],"wp:attachment":[{"href":"https:\/\/m.kawasaki-m.ac.jp\/mgm-lyso\/index.php?rest_route=%2Fwp%2Fv2%2Fmedia&parent=727"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/m.kawasaki-m.ac.jp\/mgm-lyso\/index.php?rest_route=%2Fwp%2Fv2%2Fcategories&post=727"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/m.kawasaki-m.ac.jp\/mgm-lyso\/index.php?rest_route=%2Fwp%2Fv2%2Ftags&post=727"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}